Lipofibromatosis of the Paravertebral Soft Tissue in a Child of Two Years Old

Colangeli S, Colangeli M, Gasbarrini A, Righi A and Boriani S

Department of Orthopaedic Oncology and Reconstructive Surgery, Careggi University Hospital, Florence, Italy
Department of Musculo-Skeletal Oncology, Rizzoli Orthopaedic Institute, Bologna, Italy
Department of Oncological and Degenerative Spine Surgery, Rizzoli Orthopaedic Institute, Bologna, Italy
Surgical Pathology, Rizzoli Orthopaedic Institute, Bologna, Italy

^*Correspondance to: Colangeli S 

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Abstract:

Lipofibromatosis is a bland fibroproliferative process that invades skeletal muscle. Typically the children are affected before 8 years with a peak under 2 years old. Head, neck or thigh are the most frequently involved sites.The management strategies are different: the first, periodical clinical and imaging control with MRI to evaluate the symptoms and the size of the tumor mass; the second, to assess the feasibility and to perform chemotherapy in selected cases; the third, surgical excision of the tumor. This article reports on the youngest patient diagnosed with this rare soft tissue tumor in thoracolumbar area. In fact, according to the Authors’ knowledge, no other cases of this tumor in this localization have been presented in the literature. Our study demonstrated that surgical excision is the gold treatment choice in this tumor when feasible. In fact, the scoliosis caused by tumor stopped its evolution after its surgical excision.

Keywords:

Lipofibromatosis; Spine; Tumors

Cite the Article:

Colangeli S, Colangeli M, Gasbarrini A, Righi A, Boriani S. Lipofibromatosis of the Paravertebral Soft Tissue in a Child of Two Years Old. Clin Oncol. 2017; 2: 1262.