A 25 Year-Old Male with Cerebellar Mass: LhermitteDuclos Disease

Ulger S, Demirci H, Çeltikçi E, Kurt G, Kilic D, Karakus E, Helvaci A, Ucar M and Uluoglu O

Department of Radiation Oncology, Gazi University, Turkey
Department of Neurosurgery, Gazi University, Turkey
Department of Pathology, Gazi University, Turkey
Department of Radiology, Gazi University, Turkey

^*Correspondance to: Sukran Ulger 

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Abstract:

We report a rare case of dysplastic cerebellar gangliocytoma also called as Lhermitte-Duclos Disease located in the cerebellum in a young male without any neurological signs. Morphologically dysplastic neurons and immunohistochemical staining with neuronal and glial markers was all diagnostic on pathology. Also a non-enhancing cerebellar hemispheric mass with a striated pattern of hyper-, and isointensity on T2-weighted images is classical findings on brain MRI. MRI findings of the lesion is Highlights 1. Dysplastic cerebellar gangliocytoma is an uncommon hamartomatous disorder. 2. The classical MRI findings of the lesion is a non-enhancing cerebellar hemispheric mass with a striated pattern of hyper-, and isointensity on T2-weighted images. 3. Keep in mind in younger patients without any neurological signs and hamartomatous lesions.

Keywords:

Lhermitte duclos disease; Cerebellar mass; Gangliocytoma

Cite the Article:

Ulger S, Demirci H, Çeltikçi E, Kurt G, Kilic D, Karakus E, et al. A 25 Year-Old Male with Cerebellar Mass: LhermitteDuclos Disease. Clin Oncol. 2016; 1: 1023.