Grace Onimoe1*, Eric Kodish1 and Richard Herman2
1Division of Pediatric Hematology and Oncology, Cleveland Clinic Children’s, Cleveland Ohio, USA
2Division of Pediatric Surgery, Cleveland Clinic Children’s, Cleveland Ohio, USA
Neuroendocrine tumors involving the appendix in young people are uncommon. A retrospective review of appendiceal NET at Cleveland Clinic Children’s was completed, 14 patients were identified, 3 cases were classified as intermediate grade tumors, lymph node metastasis was present in 2 cases. The largest size tumor measured 4.5 cm, 5 patients underwent right hemicolectomy per NANETS criteria, 3 patients who met this criteria did not undergo hemicolectomy. No disease recurrence. Appendiceal NET is associated with an excellent prognosis in localized disease and has low metastatic potential. A multicenter review will be beneficial in better defining criteria for a second surgery.
Onimoe G, Kodish E, Herman R. Neuroendocrine Tumors of the Appendix in Adolescents and Young Adults. Clin Oncol. 2017; 2: 1318.